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01-02-2009 | Review

Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)

Authors: Baris Turkbey, Iclal Ocak, Kailash Daryanani, Esperanza Font-Montgomery, Linda Lukose, Joy Bryant, Maya Tuchman, Parvathi Mohan, Theo Heller, William A. Gahl, Peter L. Choyke, Meral Gunay-Aygun

Published in: Pediatric Radiology | Issue 2/2009

Abstract

ARPKD/CHF is an inherited disease characterized by non-obstructive fusiform dilatation of the renal collecting ducts leading to enlarged spongiform kidneys and ductal plate malformation of the liver resulting in congenital hepatic fibrosis. ARPKD/CHF has a broad spectrum of clinical presentations involving the kidney and liver. Imaging plays an important role in the diagnosis and follow-up of ARPKD/CHF. Combined use of conventional and high-resolution US with MR cholangiography in ARPKD/CHF patients allows detailed definition of the extent of kidney and hepatobiliary manifestations without requiring ionizing radiation and contrast agents.

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Title: Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)
Authors: Baris Turkbey
Iclal Ocak
Kailash Daryanani
Esperanza Font-Montgomery
Linda Lukose
Joy Bryant
Maya Tuchman
Parvathi Mohan
Theo Heller
William A. Gahl
Peter L. Choyke
Meral Gunay-Aygun
Publication date: 01-02-2009
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 2/2009
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-008-1064-x

2024 ASCO Annual Meeting

Springer Medicine

Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)

Abstract

2024 ASCO Annual Meeting

Springer Medicine

Abstract

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