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01-10-2006

Absent Right and Persistent Left Superior Vena Cava: Fetal and Neonatal Echocardiographic Diagnosis

Authors: G. Favia Guarnieri, F. Romano, L. Clericò, G. Balducci

Published in: Pediatric Cardiology | Issue 5/2006

Abstract

Absence of the right superior vena cava (SVC) is a rare event occurring in patients without congenital cardiovascular abnormalities. Since absence of the right SVC is usually clinically silent, its diagnosis is mandatory prior to invasive medical or surgical procedures. We report two cases of echocardiographic diagnosis of absence of the right SVC with persistent left SVC and a large coronary sinus in structurally normal heart in a fetus of 20 weeks’ gestation and in a newborn. The diagnosis was confirmed by transthoracic contrast echocardiography with intravenous injection of agitated saline into the right arm.

Bartram U, van Praagh S, Levine JC, et al. (1997) Absent right superior vena cava in visceroatrial situs solitus. Am J Cardiol 80:175–183PubMedCrossRef

Bernadis C, Chatzis A, Treausure T (1992) Absent right superior vena cava associated with disease of sinus node. Int J Cardiol 36:115–157CrossRef

Chan KL, Abdulla A (2000) Images in cardiology. Giant coronary sinus and absent right superior vena cava. Heart 83:70CrossRef

Chopra PS, Rao RS (1992) Corrective surgery for tricuspid atresia: which modification of Fontan–Kreeutzer procedure should be used? A review. Am Heart J 123:758–767PubMedCrossRef

Cochrane AD, Marath A, Mee RBB (1994) Can a dilated coronary sinus produce left ventricular inflow obstruction? An unrecognized entity. Ann Thorac Surg 58:1114–1116PubMedCrossRef

Lenox CC, Zuberbuhler JR, Park SC, et al. (1980) Absent right superior vena cava with persistent left superior vena cava: implications and management. Am J Cardiol 45:117–122PubMedCrossRef

Mooney DP, Snyder CL, Holder TM (1993) An absent right and persistent left superior vena cava in an infant requiring extracorporeal membrane oxygenation therapy. J Pediatr Surg 28:1633–1634PubMedCrossRef

Quinn RD, Myers JL, Pae WE Jr, Clemson BS, Davis D (1992) Orthotopic heart transplantation with preoperative unsuspected left superior vena cava and absence right superior vena cava. J Heart Lung Transplant 11:147–151PubMed

Rychik J, Ayres N, Cuneo B, et al. (2004) American Society of Echocardiography guidelines and standards for performance of the fetal echocardiogram. J Am Soc Echocardiogr 17:803–810PubMedCrossRef

10.

Winter FS (1954) Persistent left superior vena cava: survey of world literature and report of thirty additional cases Angiology 5:90–131PubMed

Title: Absent Right and Persistent Left Superior Vena Cava: Fetal and Neonatal Echocardiographic Diagnosis
Authors: G. Favia Guarnieri
F. Romano
L. Clericò
G. Balducci
Publication date: 01-10-2006
Publisher: Springer-Verlag
Published in: Pediatric Cardiology / Issue 5/2006
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-005-1264-1

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Absent Right and Persistent Left Superior Vena Cava: Fetal and Neonatal Echocardiographic Diagnosis

Abstract

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Abstract

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