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Pediatric Cardiology
Published in: Pediatric Cardiology 1/2005

01-02-2005

Post-hoc Diagnosis of Congenital Long QT Syndrome in Patients with Tetralogy of Fallot

Authors: J. Walls, S. Sanatani, R. Hamilton

Published in: Pediatric Cardiology | Issue 1/2005

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Abstract

This report describes two patients diagnosed with congenital long QT syndrome after surgical repair of tetralogy of Fallot. Despite the fact that both patients had preoperative electrocardiograms demonstrating QT prolongation, neither was diagnosed until long after their surgeries, when they or their relatives presented with symptoms of long QT syndrome. A brief discussion highlights the reasons why long QT syndrome may be overlooked in patients with structural heart defects and the clinical importance of identifying these patients preoperatively.
Literature
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Metadata
Title
Post-hoc Diagnosis of Congenital Long QT Syndrome in Patients with Tetralogy of Fallot
Authors
J. Walls
S. Sanatani
R. Hamilton
Publication date
01-02-2005
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 1/2005
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-004-0712-7

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