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Published in: Neuroradiology 4/2012

01-04-2012 | Diagnostic Neuroradiology

Diagnosis of neuromyelitis optica (NMO) spectrum disorders: is MRI obsolete?

Authors: Jonathan James Downer, Maria Isabel Leite, Ranjana Carter, Jacqueline Palace, Wilhelm Küker, Gerardine Quaghebeur

Published in: Neuroradiology | Issue 4/2012

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Abstract

Introduction

Neuromyelitis optica (NMO) is a severe demyelinating disease that preferentially involves spinal cord and optic nerve. It is part of a spectrum of neurological conditions associated with antibodies to aquaporin-4 (AQP4). This study investigates the role of MRI where novel, more sensitive AQP4 antibody immunoassay techniques are being used.

Methods

Retrospective review of neuroimaging in 69 patients (25 antibody positive, 44 antibody negative), investigated in the context of suspected NMO or NMO spectrum disorder, was performed independently by two consultant neuroradiologists.

Results

Longitudinally extensive, central spinal cord lesions were more frequent in AQP4 positive patients (95.2% vs 35.5%, p < 0.0001; 85.7% vs 45.2%, p = 0.015). Multiple sclerosis diagnostic criteria were less frequently fulfilled on brain MRI in antibody positive patients (5.6% vs 33.3%, p = 0.035). Juxtacortical and corpus callosal lesions were also less common in this group (16.7% vs 46.7%, p = 0.063; 5.6% vs 46.7%, p = 0.0034). Hypothalamic and periependymal disease related to the aqueduct was not seen in antibody negative patients. T1 hypointensity was more common in cord lesions of antibody positive patients (75.0% vs 35.3%, p = 0.037). However, this characteristic did not discriminate antibody positive and negative longitudinally extensive cord lesions (73.3% vs 62.5%, p = 0.66).

Conclusion

The NMO spectrum of diseases are among an increasing number of neurological conditions defined by serological tests. However, despite improved immunoassay techniques, MRI of the brain and spinal cord continues to be among the first-line investigations in these patients, providing valuable diagnostic information that will help guide patient management.
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Metadata
Title
Diagnosis of neuromyelitis optica (NMO) spectrum disorders: is MRI obsolete?
Authors
Jonathan James Downer
Maria Isabel Leite
Ranjana Carter
Jacqueline Palace
Wilhelm Küker
Gerardine Quaghebeur
Publication date
01-04-2012
Publisher
Springer-Verlag
Published in
Neuroradiology / Issue 4/2012
Print ISSN: 0028-3940
Electronic ISSN: 1432-1920
DOI
https://doi.org/10.1007/s00234-011-0875-x

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