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Obesity Surgery
Published in: Obesity Surgery 10/2008

01-10-2008 | Research Article

Launois-Bensaude Syndrome: An Unusual Localization of Obesity Disease

Authors: Giovanni Verna, Nicola Kefalas, Filippo Boriani, Salvatore Carlucci, Ingrid Choc, Maria Alessandra Bocchiotti

Published in: Obesity Surgery | Issue 10/2008

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Abstract

Background

Launois-Bensaude syndrome is a rare pathology consisting of adipose masses symmetrically distributed mainly in the superior part of the body. Men are especially affected between age of 30 and 60 as well as chronic alcohol abusers. Etiopathogenesis is attributable to mutations or deletions of mitochondrial DNA, and alcohol is a possible cofactor.

Methods

The current treatment of the disease is described based on the authors’ experience. Four cases treated in our department are retrospectively reviewed regarding comorbidities and type of surgery performed.

Results

A relevant and long-lasting reduction of fat bulges has been obtained in all cases with no major complications except for a mild anemia.

Conclusion

Launois-Bensaude syndrome causes a functional rather than esthetic concern due to the peculiar localization of fat bulges. Currently, the only effective therapy is surgery, through lipectomy or liposuction of adipose bulges.
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Metadata
Title
Launois-Bensaude Syndrome: An Unusual Localization of Obesity Disease
Authors
Giovanni Verna
Nicola Kefalas
Filippo Boriani
Salvatore Carlucci
Ingrid Choc
Maria Alessandra Bocchiotti
Publication date
01-10-2008
Publisher
Springer-Verlag
Published in
Obesity Surgery / Issue 10/2008
Print ISSN: 0960-8923
Electronic ISSN: 1708-0428
DOI
https://doi.org/10.1007/s11695-008-9502-2

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