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Published in: Clinical Orthopaedics and Related Research® 5/2011

01-05-2011 | Symposium: Myelomeningocele

Kyphectomy Improves Sitting and Skin Problems in Patients with Myelomeningocele

Authors: Sumeet Garg, MD, Matthew Oetgen, MD, Karl Rathjen, MD, B. Stephens Richards, MD

Published in: Clinical Orthopaedics and Related Research® | Issue 5/2011

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Abstract

Background

Progressive kyphosis occurs in up to 20% of patients with myelomeningocele. Severely affected patients can develop recurrent skin breakdown, osteomyelitis, sitting imbalance, and poor cosmetic appearance.

Questions/purposes

We (1) assessed the ability of kyphectomy to restore an intact skin envelope and allow comfortable seating in a wheelchair; (2) reviewed the complications of kyphectomy and spinal fusion in myelomeningocele; and (3) determined whether patients requiring unexpected reoperation had worse correction or more ulceration compared with those patients treated with a single surgery.

Methods

We retrospectively reviewed the records of 23 children with thoracic-level myelomeningocele who were treated with kyphectomy and spinal fusion since 1980. Indications for surgery included recurrent skin breakdown (15 patients) and poor sitting balance or unacceptable cosmetic deformity (three patients). We evaluated operative technique, type of sacropelvic fixation, surgical complications, radiographic correction, and skin condition at followup. The minimum followup was 2 years (median, 4.1 years; range, 2.1–10 years); 18 of the 23 children had greater than 2 years followup and are reported here.

Results

Kyphectomy achieved a sitting balance and resolved in skin ulceration in 17 of 18 patients. Seven patients had complications requiring reoperation. Three patients had multiple reoperations for early deep infection and one patient each had reoperation for late infection, pseudarthrosis, implant-related sacral pressure sore, and planned extension of proximal fusion after growth. Patients requiring multiple operations had similar correction and relief of ulceration to those treated with a single procedure.

Conclusions

Complications after kyphectomy are frequent and many children with myelomeningocele and severe hyperkyphosis require multiple procedures and lengthy hospital stays. Nonetheless, improved seating balance and resolution of skin problems was achieved in 17 of 18 patients.

Level of Evidence

Level IV, therapeutic study. See Guidelines for Authors for a complete description of levels of evidence.
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Metadata
Title
Kyphectomy Improves Sitting and Skin Problems in Patients with Myelomeningocele
Authors
Sumeet Garg, MD
Matthew Oetgen, MD
Karl Rathjen, MD
B. Stephens Richards, MD
Publication date
01-05-2011
Publisher
Springer-Verlag
Published in
Clinical Orthopaedics and Related Research® / Issue 5/2011
Print ISSN: 0009-921X
Electronic ISSN: 1528-1132
DOI
https://doi.org/10.1007/s11999-010-1650-8

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