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Orphanet Journal of Rare Diseases
Published in: Orphanet Journal of Rare Diseases 1/2023

Open Access 01-12-2023 | Juvenile Rheumatoid Arthritis | Research

Well-being in chronic pediatric inflammatory rheumatic diseases: the experience of a French healthcare network

Authors: Rita El Haddad, Khalil El Asmar, Chrystelle Hascoët, Linda Rossi-Semerano, Perrine Dusser

Published in: Orphanet Journal of Rare Diseases | Issue 1/2023

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Abstract

Objective

Current management of patients with pediatric rheumatic diseases (PRD) should aim at achieving the best possible well-being.
To identify sociodemographic/clinical characteristics, needed paramedical services and school accommodations associated with well-being in patients at inclusion in a French health network Réseau pour les Rhumatismes Inflammatoires Pédiatriques (RESRIP) that supports coordination of the patient’s health pathway. To evaluate the evolution of well-being over time in this patients benefiting from such support.

Methods

Patients > 3 years old enrolled in RESRIP (2013–2020) were included. At enrollment, data were collected on sociodemographic/clinical characteristics, ongoing medications, and paramedical and educational actions to be implemented by RESRIP. Well-being during the last 6 months was reported with a standardized questionnaire at enrollment and every 6 months. A well-being score was calculated with scores ranging from 0 to 18, 18 corresponding to absolute well-being. Patients were followed up from inclusion until June 2020.

Results

In total, 406 patients were included and followed up for 36 months on average: 205 juvenile idiopathic arthritis, 68 connective tissue diseases, 81 auto-inflammatory diseases and 52 other diseases. The well-being score did not differ between the groups and improved significantly, by 0.04 score units, every 6 months (95% confidence interval [0.03; 0.06]). At inclusion, use of homeopathy, need for implementation of hypnosis or psychological support, occupational therapy or for adjustment of school tests were associated with worse well-being score.

Conclusion

Well-being seems associated more with the impact of chronic illness than the type of PRD underlining the importance of a comprehensive patient care.
Appendix
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Metadata
Title
Well-being in chronic pediatric inflammatory rheumatic diseases: the experience of a French healthcare network
Authors
Rita El Haddad
Khalil El Asmar
Chrystelle Hascoët
Linda Rossi-Semerano
Perrine Dusser
Publication date
01-12-2023
Publisher
BioMed Central
Published in
Orphanet Journal of Rare Diseases / Issue 1/2023
Electronic ISSN: 1750-1172
DOI
https://doi.org/10.1186/s13023-023-02655-z

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