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Published in: Pediatric Nephrology 10/2009

01-10-2009 | Brief Report

Juvenile linear scleroderma with unique forms of renal involvement

Authors: Belde Kasap, Alper Soylu, Mehmet Türkmen, Yiğit Göktay, Sülen Sarıoğlu, Can Öztürk, Özgür Kasapçopur, Salih Kavukcu

Published in: Pediatric Nephrology | Issue 10/2009

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Abstract

Linear scleroderma is the most common type of juvenile localized scleroderma, which usually involves the limbs. The linear lesions may extend through the dermis, subcutaneous tissue, muscles, and the underlying bone, leading to significant functional and cosmetic deformities. Renal involvement in juvenile localized scleroderma is a rare manifestation. Here we report two cases with juvenile linear scleroderma and unique renal manifestations, including unilateral renal arterial stenosis and immunoglobulin M nephropathy.
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Metadata
Title
Juvenile linear scleroderma with unique forms of renal involvement
Authors
Belde Kasap
Alper Soylu
Mehmet Türkmen
Yiğit Göktay
Sülen Sarıoğlu
Can Öztürk
Özgür Kasapçopur
Salih Kavukcu
Publication date
01-10-2009
Publisher
Springer Berlin Heidelberg
Published in
Pediatric Nephrology / Issue 10/2009
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI
https://doi.org/10.1007/s00467-009-1206-x

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