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Child's Nervous System

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01-03-2008 | Case Report

Intramedullary spinal arteriovenous malformation in a boy of familial cerebral cavernous hemangioma

Authors: Mei-Hua Hu, Chieh-Tsai Wu, Kuang-Lin Lin, Alex Mun-Ching Wong, Shih-Ming Jung, Chang-Teng Wu, Shao-Hsuan Hsia

Published in: Child's Nervous System | Issue 3/2008

Abstract

Object

The coexistence of spinal arteriovenous malformation (AVM) and a familial cerebral cavernous hemangioma (CCH) is extremely rare.

Methods

A 9-year-old boy suddenly developed severe paraplegia and urinary dysfunction. Spinal magnetic resonance imaging (MRI) scan revealed a cervical and upper thoracic intramedullary lesion. Due to acute neurological dysfunction, the patient underwent emergency surgical exploration. An intramedullary vascular lesion was found and excised. Pathologically, AVM was noted. After the surgery, the boy was ambulatory with left lower limb stiffness. MRI scan of the brain revealed multiple cerebral cavernous hemangioma. Symptomatic multiple CCH in his mother and grandmother were also noted.

Conclusions

We concluded that the presence of spinal AVM should be suspected if the patient with familial CCH develops the signs of space-occupying lesion of the spinal cord, facilitating early diagnosis of the spinal AVM.

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Title: Intramedullary spinal arteriovenous malformation in a boy of familial cerebral cavernous hemangioma
Authors: Mei-Hua Hu
Chieh-Tsai Wu
Kuang-Lin Lin
Alex Mun-Ching Wong
Shih-Ming Jung
Chang-Teng Wu
Shao-Hsuan Hsia
Publication date: 01-03-2008
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 3/2008
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-007-0536-x

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Intramedullary spinal arteriovenous malformation in a boy of familial cerebral cavernous hemangioma

Abstract

Object

Methods

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Object

Methods

Conclusions

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