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01-10-2003 | Case Report

Intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia

Authors: N. Orpen, R. Goodman, C. Bowker, K. Lakhoo

Published in: Pediatric Surgery International | Issue 8/2003

Abstract

Pulmonary sequestration and congenital cystic adenomatous malformations (CCAM) are well known but still uncommon anomalies of the lung. Extralobar sequestrations are well described in association with CCAM, but fewer intralobar lesions are found with this association. The existence of striated muscle within CCAM is described, and we have evidence of dysplastic changes within the various cellular components occurring, with rhabdomyomatous dysplasia being one of these. A literature review shows no previous evidence of a reported intralobar sequestration associated with CCAM and rhabdomyomatous dysplastic changes.

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Title: Intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia
Authors: N. Orpen
R. Goodman
C. Bowker
K. Lakhoo
Publication date: 01-10-2003
Publisher: Springer-Verlag
Published in: Pediatric Surgery International / Issue 8/2003
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-003-1040-3

At a glance: The STEP trials

Springer Medicine

Intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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