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Published in: European Journal of Pediatrics 2/2018

01-02-2018 | Original Article

Implications of a paediatrician-psychologist tandem for sickle cell disease care and impact on cognitive functioning

Authors: Adrienne Lerner, Hervé Picard, Adrien May, Vincent Gajdos, Louise Malou-Dhaussy, Flaviana Maroja-Cox, Laurence Salomon, Marie-Hélène Odièvre

Published in: European Journal of Pediatrics | Issue 2/2018

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Abstract

Sickle cell disease (SCD), a life-threatening chronic disease, necessitates a paediatric treatment plan that considers the influence of psychological, family and intercultural factors. At the Louis-Mourier Hospital (APHP) in Colombes, France, we introduced an original paediatric-psychological partnership where a clinical psychologist accompanies the paediatrician at programmed consultations. We evaluated children and their parents treated in Colombes and in two other paediatric units using standardized culture-free tools and clinical interviews to evaluate the psychological repercussions of SCD. We first present a global view of the different ways that SCD affects both children and their families. We then discuss findings from a study evaluating the overall efficacy of an integrated psycho-medical treatment model as compared to the usual medical care model. Children in the integrated care model improved their cognitive functioning assessed using the Rey-Osterrieth complex figure test compared to treatment as usual.
Conclusion: Findings suggest that the concept of a “partnership practice” can improve children’s ability to grapple with SCD and is a promising approach for long-term care of SCD.
What is Known:
Painful crises of sickle cell disease are unpredictable and appear in early childhood
Stress as well as the complex psychological and intercultural issues associated with SCD may aggravate the children’s symptoms
Standard pediatric care and research deal primarily with medical issues
What is New:
Evidence-based research examining the psychological repercussions of SCD in pediatric treatment as well as the parental distress
First study using standardized culture-free tools
Cognitive functioning improves under an innovative “partnership” model
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Metadata
Title
Implications of a paediatrician-psychologist tandem for sickle cell disease care and impact on cognitive functioning
Authors
Adrienne Lerner
Hervé Picard
Adrien May
Vincent Gajdos
Louise Malou-Dhaussy
Flaviana Maroja-Cox
Laurence Salomon
Marie-Hélène Odièvre
Publication date
01-02-2018
Publisher
Springer Berlin Heidelberg
Published in
European Journal of Pediatrics / Issue 2/2018
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI
https://doi.org/10.1007/s00431-017-3050-5

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