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Published in: Child's Nervous System 2/2020

01-02-2020 | Hamartoma | Case Report

Rare occurrence of gangliocytoma in the medulla oblongata

Authors: Radhika Mhatre, K. M. Bopanna, Praveen Ganigi, Mahadevan Anita

Published in: Child's Nervous System | Issue 2/2020

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Abstract

Gangliocytoma is an uncommon low-grade neuroepithelial tumour arising in the cerebral hemispheres, with medulla oblongata being extremely rare site of occurrence. We report a case of an 8-year-old female with recurrent vomiting, hypertension and left hemifacial spasms with a dorsally exophytic lesion arising from the medulla projecting into the fourth ventricle. She underwent excision of the lesion with intra operative cranial nerve monitoring guidance. Histopathology revealed clusters of large mature ganglion cells which were labelled by synaptophysin and CD34. Extreme rarity in this location makes clinical diagnosis and management of gangliocytoma challenging, although prompt diagnosis and total excision has a successful outcome. There are only six previous reports of gangliocytoma in the medulla oblongata.
Literature
1.
go back to reference Altman NR (1988) MR and CT characteristics of gangliocytoma: a rare cause of epilepsy in children. AJNR 9:917–921PubMed Altman NR (1988) MR and CT characteristics of gangliocytoma: a rare cause of epilepsy in children. AJNR 9:917–921PubMed
2.
go back to reference Awa R, Hanaya R, Hirano H, Francia C, Kitajima S, Arita K (2012) Gangliocytoma of the medulla oblongata demonstrating high tracer uptake on positron emission tomography. J Neurooncol 106:201–202CrossRef Awa R, Hanaya R, Hirano H, Francia C, Kitajima S, Arita K (2012) Gangliocytoma of the medulla oblongata demonstrating high tracer uptake on positron emission tomography. J Neurooncol 106:201–202CrossRef
3.
go back to reference Capper D, Hirose JT, Becker AJ, Rosenblum MK, Giannini C, Blumcke I (2016) Gangliocytoma. In: Louis DN, Ohgaki H, Wiestler OD (eds) WHO Classification of Tumours of the Central Nervous System, Revised, 4th edn. International Agency for Research on Cancer, Lyon, p 136 Capper D, Hirose JT, Becker AJ, Rosenblum MK, Giannini C, Blumcke I (2016) Gangliocytoma. In: Louis DN, Ohgaki H, Wiestler OD (eds) WHO Classification of Tumours of the Central Nervous System, Revised, 4th edn. International Agency for Research on Cancer, Lyon, p 136
4.
go back to reference Choi YH, Kim IO, Cheon JE, Kim WS, Yeon KM, Wang KC, Cho BK, Chi JG (2001) Gangliocytoma of the spinal cord: a case report. Pediatr Radiol 31:377–380CrossRef Choi YH, Kim IO, Cheon JE, Kim WS, Yeon KM, Wang KC, Cho BK, Chi JG (2001) Gangliocytoma of the spinal cord: a case report. Pediatr Radiol 31:377–380CrossRef
5.
go back to reference Delande O, Rodriguez D, Chiron C, Fohlen M (2001) Successful surgical relief of seizures associated with hamartoma of the floor of the fourth ventricle in children: report of two cases. Neurosurgery 49(3):726–730PubMed Delande O, Rodriguez D, Chiron C, Fohlen M (2001) Successful surgical relief of seizures associated with hamartoma of the floor of the fourth ventricle in children: report of two cases. Neurosurgery 49(3):726–730PubMed
6.
go back to reference Koerbel A, Prevedello D, Tatsui C, Pellegrino L, Hanel R, Bleggi-Torres L, Araújo JC (2003) Posterior fossa gangliocytoma with facial nerve invasion: case report. Arq Neuropsiquiatr 61:274–276CrossRef Koerbel A, Prevedello D, Tatsui C, Pellegrino L, Hanel R, Bleggi-Torres L, Araújo JC (2003) Posterior fossa gangliocytoma with facial nerve invasion: case report. Arq Neuropsiquiatr 61:274–276CrossRef
7.
go back to reference Makary R, Mohammadi A, Shuja S (2008) Glioneuronal hamartoma with unusual clinical manifestations in a case of pharmacoresistant temporal lobe epilepsy. Internet J Neurol 11(2):1–5 Makary R, Mohammadi A, Shuja S (2008) Glioneuronal hamartoma with unusual clinical manifestations in a case of pharmacoresistant temporal lobe epilepsy. Internet J Neurol 11(2):1–5
8.
go back to reference McCrory PR, Bladin PF, Berkovic SF (1999) The cerebellar seizures of Hughlings Jackson. Neurology 52(9):1888–1890CrossRef McCrory PR, Bladin PF, Berkovic SF (1999) The cerebellar seizures of Hughlings Jackson. Neurology 52(9):1888–1890CrossRef
10.
go back to reference Odia Y (2016) Gangliocytomas and gangliogliomas: review of clinical, pathologic and genetic features. Clin Oncol 1:1–6 Odia Y (2016) Gangliocytomas and gangliogliomas: review of clinical, pathologic and genetic features. Clin Oncol 1:1–6
11.
go back to reference Prayson RA (2006) Ganglion cell tumours: gangliocytoma, ganglioglioma and anaplastic ganglioglioma. In: McLendon RE, Rosenblum MK, Bigner DD (eds) Russell and Rubinstein’s Pathology of Tumors of the Nervous System, 7th edn. Hodder Arnold, London, pp 321–331 Prayson RA (2006) Ganglion cell tumours: gangliocytoma, ganglioglioma and anaplastic ganglioglioma. In: McLendon RE, Rosenblum MK, Bigner DD (eds) Russell and Rubinstein’s Pathology of Tumors of the Nervous System, 7th edn. Hodder Arnold, London, pp 321–331
12.
go back to reference Sharma M, Suri A, Shah T, Ralte A, Sarkar C, Gupta V, Mehta VS (2005) Intraventricular glioneuronal hamartoma: histopathological correlation with magnetic resonance spectroscopy. J Neuro-Oncol 74:325–328CrossRef Sharma M, Suri A, Shah T, Ralte A, Sarkar C, Gupta V, Mehta VS (2005) Intraventricular glioneuronal hamartoma: histopathological correlation with magnetic resonance spectroscopy. J Neuro-Oncol 74:325–328CrossRef
13.
go back to reference Southall DP, Lewis GM, Buchanan R, Weller RO (1987) Prolonged expiratory apnoea (cyanotic ‘breath-holding’) in association with a medullary tumour. Dev Med Child Neurol 29:789–793CrossRef Southall DP, Lewis GM, Buchanan R, Weller RO (1987) Prolonged expiratory apnoea (cyanotic ‘breath-holding’) in association with a medullary tumour. Dev Med Child Neurol 29:789–793CrossRef
14.
go back to reference Stefani FH, Mehraein P (1971) Gangliocytoma of the medulla oblongata. Arch Psychiatr Nervenkr 214:107–115CrossRef Stefani FH, Mehraein P (1971) Gangliocytoma of the medulla oblongata. Arch Psychiatr Nervenkr 214:107–115CrossRef
15.
go back to reference Takahashi M, Kondo T, Morichika M, Kuse A, Nakagawa K, Asano M et al (2016) Autopsy case of undiagnosed gangliocytoma in the medulla oblongata complicated with cerebral palsy. Legal Med 19:119–121CrossRef Takahashi M, Kondo T, Morichika M, Kuse A, Nakagawa K, Asano M et al (2016) Autopsy case of undiagnosed gangliocytoma in the medulla oblongata complicated with cerebral palsy. Legal Med 19:119–121CrossRef
16.
go back to reference Wakao N, Imagama S (2012) Intramedullary gangliocytoma with calcification and multiple intramedullary cysts. Neuroradiology 54:893–895CrossRef Wakao N, Imagama S (2012) Intramedullary gangliocytoma with calcification and multiple intramedullary cysts. Neuroradiology 54:893–895CrossRef
17.
go back to reference Zulch KJ (1979) Histological typing of tumours of the central nervous system. World Health Organization, Geneva Zulch KJ (1979) Histological typing of tumours of the central nervous system. World Health Organization, Geneva
Metadata
Title
Rare occurrence of gangliocytoma in the medulla oblongata
Authors
Radhika Mhatre
K. M. Bopanna
Praveen Ganigi
Mahadevan Anita
Publication date
01-02-2020
Publisher
Springer Berlin Heidelberg
Keyword
Hamartoma
Published in
Child's Nervous System / Issue 2/2020
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-019-04392-w

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