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Head and Neck Pathology
Published in: Head and Neck Pathology 4/2020

01-12-2020 | Hamartoma | Sine qua non Radiology-Pathology

Nasal Chondromesenchymal Hamartoma

Authors: Balamurugan Thirunavukkarasu, Debajyoti Chatterjee, Satyawati Mohindra, Bishan Dass Radotra, Shiv Jee Prashant

Published in: Head and Neck Pathology | Issue 4/2020

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Abstract

Nasal chondromesenchymal hamartoma (NCMH) is a rare, benign lesion of the sinonasal tract. It usually presents as a polypoid mass in infants and older children. Imaging studies and endoscopy are required to delineate the extent of the lesion and aid in its excision. This unusual lesion is composed of proliferating mesenchymal and cartilaginous elements. Recently, a genetic association between NCMH and DICER1 mutation has been established. It is important for pathologists to be familiar with this entity to avoid misdiagnosis since the lesion is benign and surgical excision is curative.
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Metadata
Title
Nasal Chondromesenchymal Hamartoma
Authors
Balamurugan Thirunavukkarasu
Debajyoti Chatterjee
Satyawati Mohindra
Bishan Dass Radotra
Shiv Jee Prashant
Publication date
01-12-2020
Publisher
Springer US
Keyword
Hamartoma
Published in
Head and Neck Pathology / Issue 4/2020
Electronic ISSN: 1936-0568
DOI
https://doi.org/10.1007/s12105-020-01179-3

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