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Journal of Medical Case Reports

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Open Access 01-12-2023 | Granulomatosis with Polyangiitis | Case report

Unilateral diaphragmatic palsy and pleuropericarditis in a patient with granulomatosis with polyangiitis: a case report

Authors: Ujjwol Prasad Risal, Raju Prasad Pangeni, Rakshya Pandey, Pradeep Raj Regmi, Aditi Karki, Avish Shah

Published in: Journal of Medical Case Reports | Issue 1/2023

Abstract

Background

Granulomatosis with polyangiitis (GPA) is a rare small vessel vasculitis predominantly affecting upper and lower respiratory tract and kidneys. Unilateral diaphragmatic palsy could be a rare manifestation of GPA. Here we report a case of GPA in a 45-year-old male with unilateral diaphragmatic palsy with pleuropericarditis.

Case presentation

We report a case of a 45-year-old Khas male who presented with acute onset chest pain and shortness of breath who had elevated right hemidiaphragm, bilateral pleural effusion and pericardial effusion who was later diagnosed as GPA.

Conclusions

GPA should be suspected in all patients with diaphragmatic palsy and pleuropericarditis with appropriate clinical and laboratory picture.

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Title: Unilateral diaphragmatic palsy and pleuropericarditis in a patient with granulomatosis with polyangiitis: a case report
Authors: Ujjwol Prasad Risal
Raju Prasad Pangeni
Rakshya Pandey
Pradeep Raj Regmi
Aditi Karki
Avish Shah
Publication date: 01-12-2023
Publisher: BioMed Central
Keywords: Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Vasculitis
Vasculitis
Published in: Journal of Medical Case Reports / Issue 1/2023
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-023-04105-7

At a glance: The STEP trials

Springer Medicine

Unilateral diaphragmatic palsy and pleuropericarditis in a patient with granulomatosis with polyangiitis: a case report

Abstract

Background

Case presentation

Conclusions

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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