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01-04-2004 | Original article

Getting the GIST of the Carney Triad: Growth Factors, Rare Tumors, and Cellular Respiration

Author: Paul S. Amieux

Published in: Pediatric and Developmental Pathology | Issue 4/2004

Excerpt

In this issue, Boccon-Gibod and colleagues report twins, one with paraganglioma and the other with gastrointestinal stromal tumor (GIST). These rare neoplasms may represent manifestations of the Carney Triad (GIST, functioning extra-adrenal paraganglioma, and pulmonary chondroma), an autosomal dominant disorder due to mutation(s) of a yet to be identified gene [1]. …

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Title: Getting the GIST of the Carney Triad: Growth Factors, Rare Tumors, and Cellular Respiration
Author: Paul S. Amieux
Publication date: 01-04-2004
Publisher: Springer-Verlag
Published in: Pediatric and Developmental Pathology / Issue 4/2004
Print ISSN: 1093-5266
Electronic ISSN: 1615-5742
DOI: https://doi.org/10.1007/s10024-004-4038-5

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