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01-09-2015 | Case Report

Gastric Gist with Syncronous Ampullary Gangliocytic Paraganglyoma: A Novel Presentation of an Incomplete Carney’s Triad

Authors: Marco A. Juarez-Parra, Eduardo A. Guzman-Huerta, Gerardo Ochoa-Rodriguez, Jesús Limon-Rodriguez, Zaire Zamudio-Vazquez, Luis Gregorio Osoria-Alba, Maria Jose González-Salazar, Jessica S. Cordova-Chavez

Published in: Journal of Gastrointestinal Cancer | Issue 3/2015

Excerpt

Carney’s triad is a rare multi-centric and multi-focal combination of soft tissue tumors first described in 1977 [1]; it includes the combination of gastric gastrointestinal stromal tumor (GIST), pulmonary chondromas, and extra-adrenal paraganglioma [2]. Further observations have now included the esophageal leiomyoma and the adrenal adenoma as part of the syndrome [3]. The triad is incomplete in 78 % of the cases with only two of the three tumors occurring [4]; approximately only 100 cases have been reported. Here in, we present the case of a 70-year-old man diagnosed with synchronous gastric GIST and gangliocytic paraganglioma of the ampulla of Vater. …

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Title: Gastric Gist with Syncronous Ampullary Gangliocytic Paraganglyoma: A Novel Presentation of an Incomplete Carney’s Triad
Authors: Marco A. Juarez-Parra
Eduardo A. Guzman-Huerta
Gerardo Ochoa-Rodriguez
Jesús Limon-Rodriguez
Zaire Zamudio-Vazquez
Luis Gregorio Osoria-Alba
Maria Jose González-Salazar
Jessica S. Cordova-Chavez
Publication date: 01-09-2015
Publisher: Springer US
Published in: Journal of Gastrointestinal Cancer / Issue 3/2015
Print ISSN: 1941-6628
Electronic ISSN: 1941-6636
DOI: https://doi.org/10.1007/s12029-015-9717-0

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