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Published in: Child's Nervous System 6/2018

01-06-2018 | Original Paper

Frontoethmoidal encephalocele: clinical presentation, diagnosis, treatment, and complications in 400 cases

Authors: Muhammad Arifin, Wihasto Suryaningtyas, Abdul Hafid Bajamal

Published in: Child's Nervous System | Issue 6/2018

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Abstract

Purpose

The purpose of this study is to review a large series of frontoethmoidal encephalocele (FEE) regarding their clinical presentation, the progressiveness of the mass volume, the skin stigmata as well as its surgical approach and post-surgical complications.

Method

Records of all FEE patients treated in Soetomo General Hospital, Surabaya, and Charity Foundation Program from 2008 to 2015 were reviewed. Detailed patient’s demography, clinical findings, radiology results, operative procedures, and complications were documented. Follow-up was organized in weekly basis for the first 1 month after surgery or more often when situation or complication occurred. Wound healing, neurological assessment for new or progressive deficit, pseudomeningocele, skin breakdown, cerebrospinal fluid (CSF) leakage, exposed implant, recurrent mass, and cosmetic results were documented. Since most of the patients had no direct phone line at their hometown, we relied on social worker to contact them.

Results

One-stage surgery was performed for 400 patients with FEE (212 were male and 188 were female). Of 400 patients, 388 (97%) were younger than 18 years old. Most FEEs were nasoethmoidal, either isolated or combined with nasoorbital type (347 cases [86.75%]); nasofrontal subtypes were seen in 34 cases (8.5%) and nasoorbital in 14 cases (1.5%). The mean operative time was 2 h (range 30 min–3 h). There were only two patients (0.5%) needed postoperative blood transfusions. Mean hospitalization time was 5 days (range 4–7 days). Overall, complication rate in our series was 12.5%, mostly was CSF leakage and wound dehiscence.

Conclusion

The current socioeconomic conditions and local facility should be considered to treat these specific disease processes. The refined and meticulous technique, especially in choosing the approach and handling the dural closure, is essential in lowering the complication rate.
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Metadata
Title
Frontoethmoidal encephalocele: clinical presentation, diagnosis, treatment, and complications in 400 cases
Authors
Muhammad Arifin
Wihasto Suryaningtyas
Abdul Hafid Bajamal
Publication date
01-06-2018
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 6/2018
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-017-3716-3

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