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Archives of Orthopaedic and Trauma Surgery

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01-06-2010 | Osteoporotic Fracture Management

Fractures in proximal spinal muscular atrophy

Authors: Albert Fujak, Carsten Kopschina, Raimund Forst, Florian Gras, Lutz Arne Mueller, Jürgen Forst

Published in: Archives of Orthopaedic and Trauma Surgery | Issue 6/2010

Abstract

Introduction

Fractures are a common problem for patients with spinal muscular atrophy (SMA).

Patients

A total of 131 patients with proximal SMA with an average age of 13.2 ± 9.2 years (0.7–65.6) were evaluated retrospectively. In 60 patients 94 different fractures were observed. The group consisted of 11 patients with type Ib, 81 with type II, 33 with type IIIa, 4 with IIIb and 2 with type IV. 38 of 81 SMA II patients and 17 of 33 SMA IIIa patients had suffered fractures at an average age of 8.3 ± 5.3 years (0.0–25.1) (SMA II) and 9.3 ± 6.0 years (0.0–22.1) (SMA IIIa).

Results

The most frequent fractures were of the femur (50), usually distal, of the lower leg and ankle (15), and upper arm (9). The distribution of fractures was different in SMA II and SMA IIIa. Most of the fractures could be treated conservatively. Only two femoral shaft fractures, one upper arm and a lower arm fracture were treated surgically by osteosynthesis.

Conclusion

Competent fracture treatment is an important part of the orthopaedic care of SMA patients.

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Title: Fractures in proximal spinal muscular atrophy
Authors: Albert Fujak
Carsten Kopschina
Raimund Forst
Florian Gras
Lutz Arne Mueller
Jürgen Forst
Publication date: 01-06-2010
Publisher: Springer-Verlag
Published in: Archives of Orthopaedic and Trauma Surgery / Issue 6/2010
Print ISSN: 0936-8051
Electronic ISSN: 1434-3916
DOI: https://doi.org/10.1007/s00402-010-1096-1

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Fractures in proximal spinal muscular atrophy

Abstract

Introduction

Patients

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Introduction

Patients

Results

Conclusion

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