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Published in: Journal of Medical Case Reports 1/2014

Open Access 01-12-2014 | Case report

Four successful pregnancies in a woman after Fontan palliation: a case report

Authors: Rym Gribaa, Mehdi Slim, Sana Ouali, Elies Neffati, Fehmi Remadi, Essia Boughzela

Published in: Journal of Medical Case Reports | Issue 1/2014

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Abstract

Introduction

A Fontan operation is performed to provide palliation for patients with many forms of highly complex congenital heart disease that cannot support a biventricular circulation. Increasing numbers of women who have undergone these connections in childhood are now reaching their childbearing years, and some are becoming pregnant. The low flow and fixed cardiac output of a Fontan circulation poses several problems during pregnancy.

Case presentation

We report the case of four successful pregnancies in a 31-year-old Tunisian woman with congenital tricuspid atresia after Fontan operation. Her pregnancies resulted in delivery of four healthy neonates. Her clinical status remained unchanged.

Conclusions

This case suggests that patients after adequate Fontan palliation could complete pregnancy without long-term cardiac sequelae. Intensive care should be provided with specialists, including a neonatologist, anesthesiologist and cardiologist.
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Metadata
Title
Four successful pregnancies in a woman after Fontan palliation: a case report
Authors
Rym Gribaa
Mehdi Slim
Sana Ouali
Elies Neffati
Fehmi Remadi
Essia Boughzela
Publication date
01-12-2014
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2014
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-8-350

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