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Published in: Journal of Medical Case Reports 1/2010

Open Access 01-12-2010 | Case report

Fibromuscular dysplasia presenting as a renal infarction: a case report

Authors: Annelies Van den Driessche, Erik Van Hul, Malika Ichiche, Gert A Verpooten, Jean-Louis Bosmans

Published in: Journal of Medical Case Reports | Issue 1/2010

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Abstract

Introduction

Fibromuscular dysplasia is a non-atherosclerotic, non-inflammatory disease that most commonly affects the renal and internal carotid arteries.

Case presentation

We present the case of a 44-year-old Caucasian man who was admitted with complaints of loin pain and hypertension. A computed tomography scan of the abdomen revealed a right renal infarction with a nodular aspect of the right renal artery. Subsequent renal angiography revealed a typical 'string of beads' pattern of the right renal artery with thrombus formation. Oral anticoagulation was started and the secondary hypertension was easily controlled with anti-hypertensive drugs. At follow-up, our patient refused percutaneous transluminal renal angioplasty as a definitive treatment.

Conclusions

Fibromuscular dysplasia is the most common cause of renovascular hypertension in patients under 50 years of age. Presentation with renal infarction is rare.
In fibromuscular dysplasia, angioplasty has been proven to have, at least for some indications, an advantage over anti-hypertensive drugs. Therefore, hypertension secondary to fibromuscular dysplasia is the most common cause of curable hypertension.
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Metadata
Title
Fibromuscular dysplasia presenting as a renal infarction: a case report
Authors
Annelies Van den Driessche
Erik Van Hul
Malika Ichiche
Gert A Verpooten
Jean-Louis Bosmans
Publication date
01-12-2010
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2010
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-4-199

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