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01-05-2009 | Case Report

Fatal Cardiac Arrest Due to an Unusual Fibroma of the Pulmonary Valve

Authors: Maria G. Kiaffas, Peter G. Danias, Loukas Kaklamanis, Spyridon Rammos

Published in: Pediatric Cardiology | Issue 4/2009

Abstract

Fibroma, the second most common tumor in childhood, usually is a large solitary mass involving the ventricular septum or the left and rarely the right free ventricular wall. An unusual case of a 5.2-year-old boy with a large mass originating from the pulmonary valve is reported. The patient presented for evaluation of a murmur. Echocardiography and cardiac magnetic resonance imaging showed a large tumor extending from the distal right ventricular outflow tract through the pulmonary valve and into the main pulmonary artery causing moderate obstruction. The patient had a fatal cardiac arrest while awaiting surgery. The postmortem examination proved the tumor to be a fibroma.

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Title: Fatal Cardiac Arrest Due to an Unusual Fibroma of the Pulmonary Valve
Authors: Maria G. Kiaffas
Peter G. Danias
Loukas Kaklamanis
Spyridon Rammos
Publication date: 01-05-2009
Publisher: Springer-Verlag
Published in: Pediatric Cardiology / Issue 4/2009
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-008-9380-3

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Fatal Cardiac Arrest Due to an Unusual Fibroma of the Pulmonary Valve

Abstract

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Abstract

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