Published in:
01-12-2019 | Case Report
Extramedullary Plasmacytoma of the Pancreas Complicated with Left-Sided Portal Hypertension—a Case Report and Literature Review
Authors:
Ján Csomor, Bohuš Bunganič, Dominika Dvořáková, Petr Hříbek, Klára Kmochová, Vít Campr, Inna Tučková, Cyril Šálek, Petr Urbánek, Miroslav Zavoral
Published in:
Journal of Gastrointestinal Cancer
|
Issue 4/2019
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Excerpt
Plasma cell neoplasms (PCNs) are clonal diseases of terminally differentiated B cells, which secrete a typical monoclonal immunoglobulin called M-protein or paraprotein. They account for approximately 1% of malignant and 10–15% of hematopoietic tumors [
1]. PCN can occur as a single lesion (so-called solitary plasmacytoma) or as a multiple lesion (multiple myeloma). Solitary plasmacytomas account for only about 5% of PCNs and present mostly as a single bone lesion (solitary bone plasmacytoma), less commonly as a soft tissue mass (primary extramedullary plasmacytoma (EMP)) [
2,
3]. EMPs therefore represent approximately 3% of all PCNs [
4]. …
