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Published in: Journal of Medical Case Reports 1/2009

Open Access 01-12-2009 | Case report

Extramammary Paget's disease of the penis: a case report and review of the literature

Authors: Kingsley C Ekwueme, Hani D Zakhour, Nigel J Parr

Published in: Journal of Medical Case Reports | Issue 1/2009

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Abstract

Introduction

Extramammary Paget's disease is a rare cutaneous, slow growing, intraepithelial adenocarcinoma developing in the apocrine gland-bearing areas. Isolated Paget's disease of the penis is extremely rare.

Case presentation

We describe the case of an 87-year-old Caucasian male who presented with a non-healing erythematous plaque on the shaft of the penis previously misdiagnosed as Bowen's disease. The diagnosis was made histologically on the excised specimen and was supported by immunohistochemical staining.

Conclusion

Extramammary Paget's disease is a rare disease which can mimic various types of dermatosis. A high index of suspicion is required, combined with biopsy and immunohistochemical staining in order to make the correct diagnosis. Long-term follow-up is mandatory in these patients in order to identify and treat any subsequent recurrence or concurrent malignancy.
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Metadata
Title
Extramammary Paget's disease of the penis: a case report and review of the literature
Authors
Kingsley C Ekwueme
Hani D Zakhour
Nigel J Parr
Publication date
01-12-2009
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2009
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-3-4

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