Skip to main content
Top
Published in: Pediatric Radiology 7/2007

01-07-2007 | Case Report

Extrahepatic portosystemic shunt in congenital absence of the portal vein depicted by time-resolved contrast-enhanced MR angiography

Author: Hyun Woo Goo

Published in: Pediatric Radiology | Issue 7/2007

Login to get access

Abstract

Congenital absence of the portal vein is a rare malformation in which mesenteric and splenic venous flow bypasses the liver and drains into various sites in the systemic venous system via an extrahepatic portosystemic shunt. In an 11-year-old girl with congenital absence of the portal vein, the detailed anatomy of the extrahepatic portosystemic shunt is demonstrated by time-resolved contrast-enhanced MR angiography.
Appendix
Available only for authorised users
Literature
1.
go back to reference Morgan G, Superina R (1994) Congenital absence of the portal vein: two cases and a proposed classification system for portosystemic vascular anomalies. J Pediatr Surg 29:1239–1241PubMedCrossRef Morgan G, Superina R (1994) Congenital absence of the portal vein: two cases and a proposed classification system for portosystemic vascular anomalies. J Pediatr Surg 29:1239–1241PubMedCrossRef
2.
go back to reference Niwa T, Aida N, Tachibana K et al (2002) Congenial absence of the portal vein: clinical and radiologic findings. J Comput Assist Tomogr 26:681–686PubMedCrossRef Niwa T, Aida N, Tachibana K et al (2002) Congenial absence of the portal vein: clinical and radiologic findings. J Comput Assist Tomogr 26:681–686PubMedCrossRef
3.
go back to reference Noe JA, Pittman HC, Burton EM (2006) Congenital absence of the portal vein in a child with Turner syndrome. Pediatr Radiol 36:566–568PubMedCrossRef Noe JA, Pittman HC, Burton EM (2006) Congenital absence of the portal vein in a child with Turner syndrome. Pediatr Radiol 36:566–568PubMedCrossRef
4.
go back to reference Turkbey B, Karcaaltincaba M, Demir H et al (2006) Multiple hyperplastic nodules in the liver with congenital absence of portal vein: MRI findings. Pediatr Radiol 36:445–448PubMedCrossRef Turkbey B, Karcaaltincaba M, Demir H et al (2006) Multiple hyperplastic nodules in the liver with congenital absence of portal vein: MRI findings. Pediatr Radiol 36:445–448PubMedCrossRef
5.
go back to reference Pruessmann K, Weiger M, Scheidegger M et al (1999) SENSE: sensitivity encoding for fast MRI. Magn Reson Med 42:952–962PubMedCrossRef Pruessmann K, Weiger M, Scheidegger M et al (1999) SENSE: sensitivity encoding for fast MRI. Magn Reson Med 42:952–962PubMedCrossRef
6.
go back to reference van Vaals JJ, Brummer ME, Dixon WT et al (1993) “Keyhole” method for accelerating imaging of contrast agent uptake. J Magn Reson Imaging 3:671–675PubMedCrossRef van Vaals JJ, Brummer ME, Dixon WT et al (1993) “Keyhole” method for accelerating imaging of contrast agent uptake. J Magn Reson Imaging 3:671–675PubMedCrossRef
7.
go back to reference Muthupillai R, Vick GW III, Flamm SD et al (2003) Time-resolved contrast-enhanced magnetic resonance angiography in pediatric patients using sensitivity encoding. J Magn Reson Imaging 17:559–564PubMedCrossRef Muthupillai R, Vick GW III, Flamm SD et al (2003) Time-resolved contrast-enhanced magnetic resonance angiography in pediatric patients using sensitivity encoding. J Magn Reson Imaging 17:559–564PubMedCrossRef
8.
go back to reference Chung T (2005) Magnetic resonance angiography of the body in pediatric patients: experience with a contrast-enhanced time-resolved technique. Pediatr Radiol 35:3–10PubMedCrossRef Chung T (2005) Magnetic resonance angiography of the body in pediatric patients: experience with a contrast-enhanced time-resolved technique. Pediatr Radiol 35:3–10PubMedCrossRef
9.
go back to reference Mohrs OK, Petersen SE, Voigtlaender T et al (2006) Time-resolved contrast-enhanced MR angiography of the thorax in adults with congenital heart disease. AJR 187:1107–1114PubMedCrossRef Mohrs OK, Petersen SE, Voigtlaender T et al (2006) Time-resolved contrast-enhanced MR angiography of the thorax in adults with congenital heart disease. AJR 187:1107–1114PubMedCrossRef
10.
go back to reference Goo HW, Yang DH, Park IS et al (2007) Time-resolved three-dimensional contrast-enhanced magnetic resonance angiography in patients with Fontan operation or bidirectional cavopulmonary connection: initial experience. J Magn Reson Imaging 25:727–736PubMedCrossRef Goo HW, Yang DH, Park IS et al (2007) Time-resolved three-dimensional contrast-enhanced magnetic resonance angiography in patients with Fontan operation or bidirectional cavopulmonary connection: initial experience. J Magn Reson Imaging 25:727–736PubMedCrossRef
11.
go back to reference Kim T, Murakami T, Sugihara E et al (2004) Hepatic nodular lesions associated with abnormal development of the portal vein. AJR 183:1333–1338PubMed Kim T, Murakami T, Sugihara E et al (2004) Hepatic nodular lesions associated with abnormal development of the portal vein. AJR 183:1333–1338PubMed
12.
go back to reference Shinkai M, Ohhama Y, Nishi T et al (2001) Congenital absence of the portal vein and role of liver transplantation in children. J Pediatr Surg 36:1026–1031PubMedCrossRef Shinkai M, Ohhama Y, Nishi T et al (2001) Congenital absence of the portal vein and role of liver transplantation in children. J Pediatr Surg 36:1026–1031PubMedCrossRef
Metadata
Title
Extrahepatic portosystemic shunt in congenital absence of the portal vein depicted by time-resolved contrast-enhanced MR angiography
Author
Hyun Woo Goo
Publication date
01-07-2007
Publisher
Springer-Verlag
Published in
Pediatric Radiology / Issue 7/2007
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI
https://doi.org/10.1007/s00247-007-0475-4

Other articles of this Issue 7/2007

Pediatric Radiology 7/2007 Go to the issue

Hermes

Hermes