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Published in: Pediatric Nephrology 4/2006

01-04-2006 | Brief Report

Extra-renal Wilms’ tumour—is it different?

Authors: Jayant Sastri, Rupal Dedhia, Siddharth Laskar, Tanuja Shet, Purna Kurkure, Maryann Muckaden

Published in: Pediatric Nephrology | Issue 4/2006

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Abstract

Nephroblastomas (Wilms’ tumour) are the most common solid malignancies in childhood, but extra-renal Wilms’ tumours are rare entities, and the diagnosis is made only after surgical intervention. However, the embryogenesis and the exact mechanism of occurrence of primary ERWTs is controversial, thereby presenting a number of unanswered questions of great theoretical interests. We present three well-proven cases of extra-renal Wilms’ tumour together with a review of the literature based on its histogenesis, its behaviour and its management policies.
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Metadata
Title
Extra-renal Wilms’ tumour—is it different?
Authors
Jayant Sastri
Rupal Dedhia
Siddharth Laskar
Tanuja Shet
Purna Kurkure
Maryann Muckaden
Publication date
01-04-2006
Publisher
Springer-Verlag
Published in
Pediatric Nephrology / Issue 4/2006
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI
https://doi.org/10.1007/s00467-005-0002-5

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