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BMC Pediatrics

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Open Access 01-12-2021 | Ewing's Sarcoma | Case report

Primary pulmonary Ewing’s sarcoma: rare cause of massive hemothorax in a young girl-case report

Authors: Xuefeng Ling, Jianlin Tong, Liangliang Wang, Chuan Yao, Zhiying Chen

Published in: BMC Pediatrics | Issue 1/2021

Abstract

Background

Ewing’s sarcoma is a common malignant bone tumor in children and young adults. Rarely, extra-skeletal soft tissues and visceral organs can also be the site of origin of Ewing’s sarcoma. Primary pulmonary Ewing’s sarcoma is an extremely rare malignancy.

Case presentation

We report an unusual case of primary pulmonary Ewing’s sarcoma in a 15-year-old girl who initially presented with massive hemothorax. By histopathology evaluation of surgical biopsy specimens, the diagnosis of extraosseous Ewing’s sarcoma was confirmed by both light microscopy and immunohistochemistry. Emergency, open surgery was performed by thoracic surgery at an early stage. After 3 cycles of chemotherapy, the patient was found to be stable at follow-up examination. No more hydrothorax or other symptoms.

Conclusions

We have described an extremely rare case of primary pulmonary Ewing’s sarcoma with massive hemothorax. The patient underwent surgical resection and postoperative chemotherapy, no sign of recurrence to date as an outcome.

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Title: Primary pulmonary Ewing’s sarcoma: rare cause of massive hemothorax in a young girl-case report
Authors: Xuefeng Ling
Jianlin Tong
Liangliang Wang
Chuan Yao
Zhiying Chen
Publication date: 01-12-2021
Publisher: BioMed Central
Keywords: Ewing's Sarcoma
Ewing's sarcoma
Hemothorax
Cytostatic Therapy
Published in: BMC Pediatrics / Issue 1/2021
Electronic ISSN: 1471-2431
DOI: https://doi.org/10.1186/s12887-021-02672-6

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Primary pulmonary Ewing’s sarcoma: rare cause of massive hemothorax in a young girl-case report

Abstract

Background

Case presentation

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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