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Published in: Journal of Gastrointestinal Surgery 7/2012

01-07-2012 | Case Report

Enteropathy-Associated T Cell Lymphoma Presenting with Acute Abdominal Syndrome: a Case Report and Review of Literature

Authors: Yifan Yang, Sukhjeet S. Batth, Mingyi Chen, Dariusz Borys, Ho Phan

Published in: Journal of Gastrointestinal Surgery | Issue 7/2012

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Abstract

Introduction

Enteropathy-associated T cell lymphoma (EATL) is a rare peripheral non-Hodgkin's T cell lymphoma originating from intraepithelial T lymphocytes of the intestines. In general, this condition has a poor prognosis. A common initial presentation of this cancer which is a small intestinal perforation necessitating emergency surgery is of interest to practicing surgeons. The diagnosis is rarely made prior to pathological examination.

Methods

We report a case of a 39-year-old African American man who presented with acute abdomen and was found to have a deep necrotic ulcer of the jejunum during exploratory laparotomy.

Results

Pathological examination and laboratory results demonstrated EATL, type 2, which is not associated with celiac disease. A review of the literature on EATL is also presented.
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Metadata
Title
Enteropathy-Associated T Cell Lymphoma Presenting with Acute Abdominal Syndrome: a Case Report and Review of Literature
Authors
Yifan Yang
Sukhjeet S. Batth
Mingyi Chen
Dariusz Borys
Ho Phan
Publication date
01-07-2012
Publisher
Springer-Verlag
Published in
Journal of Gastrointestinal Surgery / Issue 7/2012
Print ISSN: 1091-255X
Electronic ISSN: 1873-4626
DOI
https://doi.org/10.1007/s11605-012-1878-6

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