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Journal of Medical Case Reports

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Open Access 01-12-2017 | Case report

Ectopic cerebellar tissue in the occipital bone: a case report

Authors: Mariko Kawashima, Masahito Kobayashi, Keisuke Ishizawa, Takamitsu Fujimaki

Published in: Journal of Medical Case Reports | Issue 1/2017

Abstract

Background

Ectopic cerebellar tissue located distantly from the normal cerebellum is very rare, and its pathophysiology remains to be elucidated.

Case presentation

We report an extremely rare case of intraosseous ectopic cerebellum detected incidentally at suboccipital craniotomy in a 46-year-old Japanese woman with hemifacial spasm. She had a small bone defect in the occipital bone, which contained a tiny area of soft tissue surrounded by cerebrospinal fluid connecting to the normal subarachnoid space through a dural opening. Histopathology demonstrated cerebellar cortex tissue consisting of molecular and granular cell layers.

Conclusions

This is the first report of glioneuronal ectopia within the skull bone separated from normal brain tissue, and it is important to distinguish this entity from other osteolytic lesions.

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Title: Ectopic cerebellar tissue in the occipital bone: a case report
Authors: Mariko Kawashima
Masahito Kobayashi
Keisuke Ishizawa
Takamitsu Fujimaki
Publication date: 01-12-2017
Publisher: BioMed Central
Published in: Journal of Medical Case Reports / Issue 1/2017
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-017-1394-0

At a glance: The STEP trials

Springer Medicine

Ectopic cerebellar tissue in the occipital bone: a case report

Abstract

Background

Case presentation

Conclusions

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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