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Published in: Journal of Cardiothoracic Surgery 1/2023

Open Access 01-12-2023 | Dyspnea | Case Report

A rare coexistence: Poland’s syndrome and cardiac angiosarcoma

Authors: Fatih Kizilyel, Rafet Gunay, Mehmet Rum, Mehmet Yilmaz, Bulend Ketenci

Published in: Journal of Cardiothoracic Surgery | Issue 1/2023

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Abstract

Poland’s syndrome, a rare genetic disorder that accompanies malignancies, musculoskeletal disorders, cardiac and genitourinary syndromes. There is no study that represents the association between cardiac angiosarcoma and Poland’s syndrome. A 24-year-old female patient previously diagnosed with Poland’s syndrome was admitted to our hospital complaining of dyspnea. Diagnostic imaging showed an irregular mass in the right atrial cavity. After successful surgery, she was discharged uneventfully and the 3rd month oncologic follow-up reveals none of residual mass. The coexistence has not been diagnosed and treated in a cardiac surgery department before. With this presentation, we aimed to contribute to the literature with this presentation, for the right and early diagnosis and management of possible new cases in the future can be diagnosed and treated correctly and early.
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Metadata
Title
A rare coexistence: Poland’s syndrome and cardiac angiosarcoma
Authors
Fatih Kizilyel
Rafet Gunay
Mehmet Rum
Mehmet Yilmaz
Bulend Ketenci
Publication date
01-12-2023
Publisher
BioMed Central
Keywords
Dyspnea
Dyspnea
Published in
Journal of Cardiothoracic Surgery / Issue 1/2023
Electronic ISSN: 1749-8090
DOI
https://doi.org/10.1186/s13019-023-02138-z

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