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01-10-2015 | GI Image

Duodeno-jejunal Intussusception with Acute Pancreatitis in Peutz-Jeghers Syndrome: The First Case Presentation in Childhood

Authors: Jiro Kimura, Kiyoshi Sasaki, Takehiro Okabayashi, Yasuo Shima, Jun Iwata, Sojiro Morita

Published in: Journal of Gastrointestinal Surgery | Issue 10/2015

Excerpt

Peutz-Jeghers syndrome (PJS) is a rare condition characterized by autosomal dominant inheritance, mucocutaneous pigmentation, and gastrointestinal hamartomatous polyps, and is a subtype of hereditary gastrointestinal polyposis.1 Among PJS, there is no difference of incidence among race and sex, and the incidence has been estimated to be 1 in 120,000–150,000 births.1 The cause of PJS is a germline mutation of STK11/LKB1 (serine/threonine kinase 11) tumor suppressor gene in most patients (70–80 %).2 …

McGarrity TJ, Kulin HE, Zaino RJ. Peutz-Jeghers syndrome. Am J Gastroenterol 2000;95:596–604.CrossRefPubMed

Zbuk KM, Eng C. Hamartomatous polyposis syndromes. Natl Clin Pract Gastroenterol Hepatol 2007;4:492–502.CrossRef

Kosuke Endo, Yasuhiro Matsukawa, Shintaku Masayuki, et al.. Learn from a case duodenojejunal intussusception. Pediatric Surgery 2012;44:578–580.

Giardiello FM, Welsh SB, Hamilton SR, et al.. Increased risk of cancer in the Peutz-Jeghers syndrome. N Engl J Med 1987;316:1511–1514.CrossRefPubMed

Title: Duodeno-jejunal Intussusception with Acute Pancreatitis in Peutz-Jeghers Syndrome: The First Case Presentation in Childhood
Authors: Jiro Kimura
Kiyoshi Sasaki
Takehiro Okabayashi
Yasuo Shima
Jun Iwata
Sojiro Morita
Publication date: 01-10-2015
Publisher: Springer US
Published in: Journal of Gastrointestinal Surgery / Issue 10/2015
Print ISSN: 1091-255X
Electronic ISSN: 1873-4626
DOI: https://doi.org/10.1007/s11605-015-2827-y

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Duodeno-jejunal Intussusception with Acute Pancreatitis in Peutz-Jeghers Syndrome: The First Case Presentation in Childhood

Excerpt

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Excerpt

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