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Published in: Neurological Sciences 5/2011

01-10-2011 | Case Report

Downbeat nystagmus, ataxia and spastic tetraparesis due to coeliac disease

Authors: Mario Habek, Iva Hojsak, Barbara Barun, Vesna V. Brinar

Published in: Neurological Sciences | Issue 5/2011

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Abstract

A 25-year-old female presented to a university neurology clinic with a 1-month history of progressive ataxia, downbeat nystagmus and spastic tetraparesis. Personal history revealed polyarthralgias and weight loss. Family history was negative. Following thorough history, laboratory, neurophysiological and MRI investigations, a diagnosis of cerebellar ataxia due to coeliac disease was done. The patient was treated with strict gluten-free diet and intravenous administration of immunoglobulins. Although there are many controversies about neurological manifestations of coeliac disease, this case pointed to strong association between these two disorders. The findings of elevated protein content in the cerebrospinal fluid with positive oligoclonal bands suggested an immune-mediated process, further supported by positive anti-endomysium antibodies and anti-transglutaminase antibodies in the cerebrospinal fluid.
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Metadata
Title
Downbeat nystagmus, ataxia and spastic tetraparesis due to coeliac disease
Authors
Mario Habek
Iva Hojsak
Barbara Barun
Vesna V. Brinar
Publication date
01-10-2011
Publisher
Springer Milan
Published in
Neurological Sciences / Issue 5/2011
Print ISSN: 1590-1874
Electronic ISSN: 1590-3478
DOI
https://doi.org/10.1007/s10072-011-0506-7

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