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Child's Nervous System

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01-01-2017 | Case Report

Development of profound Chiari I malformation and cerebellar tissue loss and resolution following shunting of posterior fossa extra-axial cyst. Case report

Authors: Rabia Khan, Peter Oakes, R. Shane Tubbs, W. Jerry Oakes

Published in: Child's Nervous System | Issue 1/2017

Abstract

Introduction

Chiari I malformation can be due to a multitude of etiologies such as craniosynostosis or hydrocephalus. A posterior fossa extra-axial cyst (PFEAC) appears to be an extremely rare cause of this form of hindbrain herniation.

Case report

Herein, we report a case of PFEAC that presented with no Chiari I malformation and then presented months later with a significant Chiari I malformation. Following shunt placement of a PFEAC, striking reversal of the Chiari malformation as well as reconstitution of the cerebellum was noted.

Conclusions

Patients with PFEAC might develop a Chiari I malformation and this might be treated with shunting of the PFEAC alone.

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Title: Development of profound Chiari I malformation and cerebellar tissue loss and resolution following shunting of posterior fossa extra-axial cyst. Case report
Authors: Rabia Khan
Peter Oakes
R. Shane Tubbs
W. Jerry Oakes
Publication date: 01-01-2017
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 1/2017
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-016-3182-3

2024 ASCO Annual Meeting

Springer Medicine

Development of profound Chiari I malformation and cerebellar tissue loss and resolution following shunting of posterior fossa extra-axial cyst. Case report

Abstract

Introduction

Case report

Conclusions

2024 ASCO Annual Meeting

Springer Medicine

Abstract

Introduction

Case report

Conclusions

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