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Head & Neck Oncology
Published in: Head & Neck Oncology 1/2011

Open Access 01-12-2011 | Review

Dermatofibrosarcoma protuberans with fibrosarcomatous transformation of the head and neck

Authors: Nikolaos Angouridakis, Panagiotis Kafas, Waseem Jerjes, Stefanos Triaridis, Tahwinder Upile, Georgios Karkavelas, Angelos Nikolaou

Published in: Head & Neck Oncology | Issue 1/2011

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Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous neoplasm associated with a high cure rate. We present a case of aggressive DFSP with fibrosarcomatous areas in the head and neck. A 28-year-old Mediterranean female presented with a 45-day history of rapidly growing cutaneous lesion of the face. Surgical biopsy confirmed the diagnosis of DFSP. Subsequently, the patient underwent wide local surgical resection, followed by reconstruction. Histopathology report revealed fibrosarcomatous transformation and the patient underwent adjuvant radiotherapy. The patient continues to be disease free at the 35-month follow-up.
Although DFSP behave as non-aggressive malignancy, surgery with complete removal of the affected area is the intervention of choice. Moreover, adjuvant treatment and follow-up of the patient is essential in order to prevent recurrence.
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Metadata
Title
Dermatofibrosarcoma protuberans with fibrosarcomatous transformation of the head and neck
Authors
Nikolaos Angouridakis
Panagiotis Kafas
Waseem Jerjes
Stefanos Triaridis
Tahwinder Upile
Georgios Karkavelas
Angelos Nikolaou
Publication date
01-12-2011
Publisher
BioMed Central
Published in
Head & Neck Oncology / Issue 1/2011
Electronic ISSN: 1758-3284
DOI
https://doi.org/10.1186/1758-3284-3-5

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