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01-08-2011 | Case Report

Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum

Authors: Pierre-Emmanuel Séguéla, Lucile Houyel, Philippe Loget, Jean-Dominique Piot, Jean-François Paul

Published in: Pediatric Radiology | Issue 8/2011

Abstract

We report the case of a newborn with pulmonary atresia with intact ventricular septum and right ventricle-dependent coronary circulation. He died several weeks after a Blalock-Taussig procedure because of a progressive stenosis of the main coronary artery. We present echocardiographic and dual-source CT images of the stenosis, with autopsy correlation. To our knowledge, CT images of this quality have never been reported in a newborn. This case illustrates the extreme difficulty in prognosticating the outcome for these patients and underlines the need for a detailed neonatal coronary mapping to assess right ventricle-dependent coronary circulation.

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Title: Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum
Authors: Pierre-Emmanuel Séguéla
Lucile Houyel
Philippe Loget
Jean-Dominique Piot
Jean-François Paul
Publication date: 01-08-2011
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 8/2011
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-011-2068-5

At a glance: The STEP trials

Springer Medicine

Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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