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Open Access 01-12-2014 | Case report

Correction of aortic coarctation in a girl with severe PHACE syndrome

Authors: Lian Xiong, Zhenkun Xia, Chengming Fan, Weizhi Zhang, Jinfu Yang

Published in: Journal of Cardiothoracic Surgery | Issue 1/2014

Abstract

A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation, and the descending aorta was distorted. Cerebrovascular revealed distorted arteries and a completely aberrant brain blood supply. She underwent correction of the aortic coarctation by establishing a bypass between the ascending aorta and the descending aorta using a 13-mm Gore-tex tube. Postoperative recovery was uneventful, at 6-month follow-up, the cervical vascular pulsatility was relieved and she is in good condition.

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Title: Correction of aortic coarctation in a girl with severe PHACE syndrome
Authors: Lian Xiong
Zhenkun Xia
Chengming Fan
Weizhi Zhang
Jinfu Yang
Publication date: 01-12-2014
Publisher: BioMed Central
Published in: Journal of Cardiothoracic Surgery / Issue 1/2014
Electronic ISSN: 1749-8090
DOI: https://doi.org/10.1186/s13019-014-0169-6

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Correction of aortic coarctation in a girl with severe PHACE syndrome

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