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Published in: Pediatric Radiology 2/2006

01-02-2006 | Case Report

Contribution of fetal MRI to the diagnosis of inner ear abnormalities: report of two cases

Authors: Bogdana Tilea, Catherine Garel, Françoise Menez, Edith Vuillard, Monique Elmaleh-Bergès, Anne-Lise Delezoide, Guy Sebag

Published in: Pediatric Radiology | Issue 2/2006

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Abstract

We report two cases of fetal inner ear abnormalities diagnosed by MRI. Cerebral MRI was performed on two fetuses, at 32 and 30 weeks gestation, following US that demonstrated multiple malformations suggestive of CHARGE syndrome in one fetus and ventriculomegaly and poor visibility of the posterior fossa in the other. MRI revealed vestibular hypoplasia and agenesis of the semicircular canals in one fetus and cystic cochleas, partial vermian agenesis and an occipital meningocele in the second fetus. Both pregnancies were terminated and there was good correlation between fetal MRI, ex utero CT and fetopathological findings. The inner ears should be carefully examined when performing fetal cerebral MRI because abnormalities of the inner ear may be associated with cerebral anomalies.
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Metadata
Title
Contribution of fetal MRI to the diagnosis of inner ear abnormalities: report of two cases
Authors
Bogdana Tilea
Catherine Garel
Françoise Menez
Edith Vuillard
Monique Elmaleh-Bergès
Anne-Lise Delezoide
Guy Sebag
Publication date
01-02-2006
Publisher
Springer-Verlag
Published in
Pediatric Radiology / Issue 2/2006
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI
https://doi.org/10.1007/s00247-005-0026-9

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