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01-04-2014 | Case Report

Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions

Authors: Maria A. Calvo-Garcia, Foong-Yen Lim, Jerzy Stanek, Constance Bitters, Beth M. Kline-Fath

Published in: Pediatric Radiology | Issue 4/2014

Abstract

We present a prenatal case of congenital peribronchial myofibroblastic tumor referred as a congenital pulmonary airway malformation (CPAM) with hydrops and polyhydramnios at 30 weeks’ gestational age. US and fetal MRI findings did not fit with the referral diagnosis, raising the possibility of intrinsic lung tumor. Fetal hydrops worsened and the baby was successfully delivered by ex utero intrapartum treatment (EXIT) to resection at 31 weeks’ gestational age. To the best of our knowledge, this is a unique case of congenital peribronchial myofibroblastic tumor that underwent comprehensive prenatal evaluation and EXIT procedure with good outcome.

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Title: Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions
Authors: Maria A. Calvo-Garcia
Foong-Yen Lim
Jerzy Stanek
Constance Bitters
Beth M. Kline-Fath
Publication date: 01-04-2014
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Radiology / Issue 4/2014
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-013-2817-8

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Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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