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Published in: Clinical Neuroradiology 3/2018

Open Access 01-09-2018 | Correspondence

Concomitant Retroperitoneal and Subarachnoid Hemorrhage Due to Segmental Arterial Mediolysis

Case Report and Review of the Literature

Authors: V. Hellstern, M. Aguilar Pérez, P. Kohlhof-Meinecke, H. Bäzner, O. Ganslandt, H. Henkes

Published in: Clinical Neuroradiology | Issue 3/2018

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Excerpt

“Segmental mediolytic arteriopathy” or “segmental arterial mediolysis” (SAM) is an up to now idiopathic disorder of the visceral and intracranial arteries and is known as a cause of major abdominal, retroperitoneal and subarachnoid hemorrhage [13]. Recently, Pickup and Pollanen [4] suggested SAM to be a condition found in Ehlers–Danlos type IV. The affected arteries show a noninflammatory and nonatherosclerotic vacuolization and lysis of the tunica media, smooth muscle degeneration and serration of the lamina elastica interna. These alterations undermine the vessel wall stability. Spontaneous dissection and aneurysm formation, followed by aneurysm rupture may occur. SAM is the most likely diagnosis in the case of simultaneous abdominal or retroperitoneal and subarachnoid hemorrhage. We describe the case history of a patient with ruptured dissecting aneurysms of abdominal and intracranial arteries. The basilar artery aneurysm was treated by endovascular flow diversion. …
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Metadata
Title
Concomitant Retroperitoneal and Subarachnoid Hemorrhage Due to Segmental Arterial Mediolysis
Case Report and Review of the Literature
Authors
V. Hellstern
M. Aguilar Pérez
P. Kohlhof-Meinecke
H. Bäzner
O. Ganslandt
H. Henkes
Publication date
01-09-2018
Publisher
Springer Berlin Heidelberg
Published in
Clinical Neuroradiology / Issue 3/2018
Print ISSN: 1869-1439
Electronic ISSN: 1869-1447
DOI
https://doi.org/10.1007/s00062-017-0641-5

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