Published in:
Open Access
01-09-2018 | Correspondence
Concomitant Retroperitoneal and Subarachnoid Hemorrhage Due to Segmental Arterial Mediolysis
Case Report and Review of the Literature
Authors:
V. Hellstern, M. Aguilar Pérez, P. Kohlhof-Meinecke, H. Bäzner, O. Ganslandt, H. Henkes
Published in:
Clinical Neuroradiology
|
Issue 3/2018
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Excerpt
“Segmental mediolytic arteriopathy” or “segmental arterial mediolysis” (SAM) is an up to now idiopathic disorder of the visceral and intracranial arteries and is known as a cause of major abdominal, retroperitoneal and subarachnoid hemorrhage [
1‐
3]. Recently, Pickup and Pollanen [
4] suggested SAM to be a condition found in Ehlers–Danlos type IV. The affected arteries show a noninflammatory and nonatherosclerotic vacuolization and lysis of the tunica media, smooth muscle degeneration and serration of the lamina elastica interna. These alterations undermine the vessel wall stability. Spontaneous dissection and aneurysm formation, followed by aneurysm rupture may occur. SAM is the most likely diagnosis in the case of simultaneous abdominal or retroperitoneal and subarachnoid hemorrhage. We describe the case history of a patient with ruptured dissecting aneurysms of abdominal and intracranial arteries. The basilar artery aneurysm was treated by endovascular flow diversion. …