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European Archives of Oto-Rhino-Laryngology

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26-02-2024 | Cochlear Implant | Case Report

Bilateral cochlear implants in a MELAS patient

Authors: Yung-Chen Sun, Yu-Pu Chou, Pei-Hsuan Ho, Xiang-Xiang Chen, Pey-Yu Chen, Chia-Huei Chu, Hung-Ching Lin

Published in: European Archives of Oto-Rhino-Laryngology | Issue 6/2024

Abstract

Background

Mitochondrial encephalopathy, lactic acidosis, and stroke-like episodes (MELAS) is a maternally inherited mitochondrial disease that affects various systems in the body, particularly the brain, nervous system, and muscles. Among these systems, sensorineural hearing loss is a common additional symptom.

Methods

A 42-year-old female patient with MELAS who experienced bilateral profound deafness and underwent bilateral sequential cochlear implantation (CIs). Speech recognition and subjective outcomes were evaluated.

Results

Following the first CI follow-up, the patient exhibited improved speech recognition ability and decided to undergo the implantation of the second ear just two months after the initial CI surgery. The second CI also demonstrated enhanced speech recognition ability. Subjective outcomes were satisfactory for bilateral CIs.

Conclusions

MELAS patients receiving bilateral CIs can attain satisfactory post-CI speech recognition, spatial hearing, and sound qualities.

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Title: Bilateral cochlear implants in a MELAS patient
Authors: Yung-Chen Sun
Yu-Pu Chou
Pei-Hsuan Ho
Xiang-Xiang Chen
Pey-Yu Chen
Chia-Huei Chu
Hung-Ching Lin
Publication date: 26-02-2024
Publisher: Springer Berlin Heidelberg
Keyword: Cochlear Implant
Published in: European Archives of Oto-Rhino-Laryngology / Issue 6/2024
Print ISSN: 0937-4477
Electronic ISSN: 1434-4726
DOI: https://doi.org/10.1007/s00405-024-08532-0

At a glance: The STEP trials

Springer Medicine

Bilateral cochlear implants in a MELAS patient

Abstract

Background

Methods

Results

Conclusions

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Methods

Results

Conclusions

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