Top

Published in:

01-05-2013 | Case Report

Circumoral complications in hereditary sensory and autonomic neuropathy — a case of simple lip reconstruction?

Authors: Tomas Madura, Alex McGrath, Kay Hood, Mamta Shah

Published in: European Journal of Plastic Surgery | Issue 5/2013

Abstract

We report a case of a 7-year-old Bangladeshi boy who caused himself oral incontinence by self-mutilation. The patient was known to suffer from hereditary sensory and autonomic neuropathy type V. As definitive management, a full dental clearance was performed along with reconstruction of the lower lip with a good functional and aesthetic outcome. He did not experience any adverse effects from the full dental clearance with regard to feeding, nutrition or development. We discuss the dilemma and challenges raised in the management of this patient and highlight the need for a multi-disciplinary specialist input for what appeared to be a simple case of lip reconstruction for a plastic surgeon.

Axelrod FB, Hilz MJ (2003) Inherited autonomic neuropathies. Semin Neurol 23:381–390PubMedCrossRef

Shaaban H, Bayat A, Davenport P, Shah M (2002) Necrotising fasciitis in an infant with congenital insensitivity to pain syndrome. Br J Plast Surg 55:160–163PubMedCrossRef

Schalka MMS, Correa MSNP, Ciamponi AL (2006) Congenital insensitivity-to-pain with anhidrosis (CIPA): A case report with 4-year follow-up. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 101:769–773PubMedCrossRef

Amano A, Akiyama S, Ikeda M, Morisaki I (1998) Oral manifestations of hereditary sensory and autonomic neuropathy type IV. Congenital insensitivity to pain with anhidrosis. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 86:425–431PubMedCrossRef

Littlewood SJ, Mitchell L (1998) The dental problems and management of a patient suffering from congenital insensitivity to pain. Int J Paediatr Dent 8:47–50PubMed

Bodner L, Woldenberg Y, Pinsk V, Levy J (2002) Orofacial manifestations of congenital insensitivity to pain with anhidrosis: a report of 24 cases. ASDC J Dent Child 69:293–6PubMed

Erdem TL, Ozcan I, Ilguy D, Sirin S (2000) Hereditary sensory and autonomic neuropathy: review and a case report with dental implications. J Oral Rehabil 27:180–183PubMedCrossRef

Butler J, Fleming P, Webb D (2006) Congenital insensitivity to pain—review and report of a case with dental implications. Oral Surg Oral Med Oral Pathol Oral Radiol Endod 101:58–62PubMedCrossRef

Thompson CC, Park RI, Prescott GH (1980) Oral manifestations of the congenital insensitivity-to-pain syndrome. Oral Surg Oral Med Oral Pathol 50:220–225PubMedCrossRef

10.

Rasmussen P (1996) The congenital insensitivity-to-pain syndrome (analgesia congenita): report of a case. Int J Paediatr Dent 6:117–122PubMedCrossRef

Title: Circumoral complications in hereditary sensory and autonomic neuropathy — a case of simple lip reconstruction?
Authors: Tomas Madura
Alex McGrath
Kay Hood
Mamta Shah
Publication date: 01-05-2013
Publisher: Springer-Verlag
Published in: European Journal of Plastic Surgery / Issue 5/2013
Print ISSN: 0930-343X
Electronic ISSN: 1435-0130
DOI: https://doi.org/10.1007/s00238-012-0704-4

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Circumoral complications in hereditary sensory and autonomic neuropathy — a case of simple lip reconstruction?

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Please log in to get access to this content

Other articles of this Issue 5/2013

Complications in immediate breast reconstruction using Strattice™

Intradermal injection of GFP-producing adipose stromal cells promotes survival of random-pattern skin flaps in rats

Chronic hematoma on the forearm mimicking soft tissue sarcoma

An anecdotal case of acute single finger ischemia in a patient with mild Raynaud’s syndrome

Use of hyaluronic acid in the correction of contour asymmetries following rhinoplasty

Adjunctive treatment of keloids: comparison of photodynamic therapy with brachytherapy