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01-01-2011 | Case Report

Chiari 1 malformation and holocord syringomyelia presenting as abrupt onset foot drop

Authors: Hugh J. McMillan, Erick Sell, Munyao Nzau, Enrique C. G. Ventureyra

Published in: Child's Nervous System | Issue 1/2011

Abstract

We present two patients with a Chiari 1 malformation and holocord syringomyelia who presented with abrupt onset unilateral foot drop. Neurophysiologic testing was consistent with a proximal nerve root lesion. This assisted with localization and directed magnetic resonance (MR) imaging to lumbosacral spine and nerve roots. Each child underwent a suboccipital craniectomy and laminectomy with duroplasty to decompress the foramen magnum. Each child also showed rapid and complete clinical recovery despite the significant electromyographic and MRI abnormalities on initial study.

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Title: Chiari 1 malformation and holocord syringomyelia presenting as abrupt onset foot drop
Authors: Hugh J. McMillan
Erick Sell
Munyao Nzau
Enrique C. G. Ventureyra
Publication date: 01-01-2011
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 1/2011
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-010-1275-y

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Chiari 1 malformation and holocord syringomyelia presenting as abrupt onset foot drop

Abstract

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Abstract

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