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01-02-2018 | Case Report - Vascular

Cerebral and spinal cavernomas associated with Klippel-Trenaunay syndrome: case report and literature review

Authors: Takaya Yoshinaga, Kenji Yagi, Takashi Morishita, Hiroshi Abe, Masani Nonaka, Tooru Inoue

Published in: Acta Neurochirurgica | Issue 2/2018

Abstract

Klippel-Trenaunay-Weber syndrome (KTWS) involves a triad of conditions, including cutaneous hemangiomas, venous varicosities, and osseous and soft-tissue hypertrophy of the affected limb. We describe a rare case of multiple cavernomas in the central nervous system in a patient with KTWS. A-64-year-old man with KTWS and a previous brain hemorrhage presented with sudden onset of gait and vesicorectal disturbance. The magnetic resonance imaging scan showed a cavernoma associated with hemorrhage in his lumbosacral spinal cord. Moreover, numerous cavernomas were identified in his brain. He was treated conservatively with no adverse events. Gait disturbance improved, but vesicorectal disturbance did not improve.

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Title: Cerebral and spinal cavernomas associated with Klippel-Trenaunay syndrome: case report and literature review
Authors: Takaya Yoshinaga
Kenji Yagi
Takashi Morishita
Hiroshi Abe
Masani Nonaka
Tooru Inoue
Publication date: 01-02-2018
Publisher: Springer Vienna
Published in: Acta Neurochirurgica / Issue 2/2018
Print ISSN: 0001-6268
Electronic ISSN: 0942-0940
DOI: https://doi.org/10.1007/s00701-017-3408-5

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Cerebral and spinal cavernomas associated with Klippel-Trenaunay syndrome: case report and literature review

Abstract

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Abstract

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