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01-02-2004 | Case Report

Cerebral anaplastic pleomorphic xanthoastrocytoma with meningeal dissemination at first presentation

Authors: Alphonse Lubansu, Sandrine Rorive, Philippe David, Eric Sariban, Roland Seligmann, Jacques Brotchi, Benoit Pirotte

Published in: Child's Nervous System | Issue 2/2004

Abstract

Introduction

Pleomorphic xanthoastrocytoma (PXA) is a rare brain glial tumour found in young patients. Most cases are reported as evolving low-grade neoplasms associated with a long survival after complete surgical resection. Some PXAs, however, can demonstrate secondary malignant transformation or progress with a short survival. Anaplastic histological features at first presentation or secondary meningeal dissemination have rarely been reported.

Case report

We describe the case of a cerebral PXA in a 7-year-old girl presenting with anaplastic histological features and craniospinal meningeal dissemination that progressed rapidly with a poor outcome.

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Title: Cerebral anaplastic pleomorphic xanthoastrocytoma with meningeal dissemination at first presentation
Authors: Alphonse Lubansu
Sandrine Rorive
Philippe David
Eric Sariban
Roland Seligmann
Jacques Brotchi
Benoit Pirotte
Publication date: 01-02-2004
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 2/2004
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-003-0854-6

2024 ASCO Annual Meeting

Springer Medicine

Cerebral anaplastic pleomorphic xanthoastrocytoma with meningeal dissemination at first presentation

Abstract

Introduction

Case report

2024 ASCO Annual Meeting

Springer Medicine

Abstract

Introduction

Case report

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