Biliary rhabdomyosarcoma

Excerpt

A 2-year-old boy was imaged for high-grade jaundice. US and CT (Fig. 1) revealed a multilocular cystic lesion at the porta hepatis. MR cholangiography demonstrated dilated bile ducts and a multilocular cystic lesion in place of the common bile duct (CBD) (Fig. 2, arrows). Percutaneous transhepatic cholangiography showed compression and obstruction of the CBD and no communication with the tumour. After biliary drainage, an open biopsy revealed the tumour to be a rhabdomyosarcoma (RMS). At the time of this report he was well 3 years after total resection of the tumour and biliary reconstruction followed by chemo- and radiotherapy.

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