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Skeletal Radiology
Published in: Skeletal Radiology 3/2009

01-03-2009 | Case Report

Atlanto-axial segmentation defects and os odontoideum in two male siblings with opsismodysplasia

Authors: Ali Al Kaissi, Farid Ben Chehida, Maher Ben Ghachem, Franz Grill, Klaus Klaushofer

Published in: Skeletal Radiology | Issue 3/2009

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Abstract

We report two siblings aged 11 and 7 years, respectively, who presented with the clinical and radiographic features of opsismodysplasia (non-lethal type). 3D computed tomography scans of the craniocervical region revealed a split atlas and os odontoideum in both siblings. To the best of our knowledge, this is the first clinical report detailing craniocervical malformations in two siblings with opsismodysplasia.
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Metadata
Title
Atlanto-axial segmentation defects and os odontoideum in two male siblings with opsismodysplasia
Authors
Ali Al Kaissi
Farid Ben Chehida
Maher Ben Ghachem
Franz Grill
Klaus Klaushofer
Publication date
01-03-2009
Publisher
Springer Berlin Heidelberg
Published in
Skeletal Radiology / Issue 3/2009
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-008-0623-4

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