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Journal of Medical Case Reports

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Open Access 01-12-2013 | Case report

Aortic aneurysm rupture as a rare complication of granulomatosis with polyangiitis: a case report

Authors: Nobuo Ohta, Takayoshi Waki, Shigeru Fukase, Yusuke Suzuki, Kazuya Kurakami, Masaru Aoyagi, Seiji Kakehata

Published in: Journal of Medical Case Reports | Issue 1/2013

Abstract

Introduction

Granulomatosis with polyangiitis is characterized by systemic inflammation of medium and small blood vessels. Aortic involvement in granulomatosis with polyangiitis is extremely rare. As far as we know this is the first reported case of successful treatment in a patient with granulomatosis with polyangiitis complicated with aortic aneurysm rupture.

Case presentation

We describe a case of granulomatosis with polyangiitis in a 38-year-old Japanese man who developed an aortic aneurysm rupture 22 years after disease onset. The patient was operated on and a J-graft was inserted. He recovered uneventfully.

Conclusion

Recommendations in regard to, and consideration of, aortic involvement should be kept in mind in the long-term careful follow up of granulomatosis with polyangiitis.

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Title: Aortic aneurysm rupture as a rare complication of granulomatosis with polyangiitis: a case report
Authors: Nobuo Ohta
Takayoshi Waki
Shigeru Fukase
Yusuke Suzuki
Kazuya Kurakami
Masaru Aoyagi
Seiji Kakehata
Publication date: 01-12-2013
Publisher: BioMed Central
Published in: Journal of Medical Case Reports / Issue 1/2013
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/1752-1947-7-202

At a glance: The STEP trials

Springer Medicine

Aortic aneurysm rupture as a rare complication of granulomatosis with polyangiitis: a case report

Abstract

Introduction

Case presentation

Conclusion

At a glance: The STEP trials

Springer Medicine

Abstract

Introduction

Case presentation

Conclusion

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