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Journal of Medical Case Reports

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Open Access 01-12-2019 | Angiography | Case report

Optical coherence tomography angiography in Purtscher-like retinopathy associated with dermatomyositis: a case report

Authors: D. Vezzola, D. Allegrini, M. R. Romano, L. Pagano, A. Montericcio, P. Fogagnolo, L. M. Rossetti, S. De Cillà

Published in: Journal of Medical Case Reports | Issue 1/2019

Abstract

Purpose

To describe a multimodal imaging diagnosis of retinopathy in dermatomyositis.

Case presentation

A 21-year-old white woman with a history of fatigue and a cutaneous rash complained of visual impairment in her left eye. A funduscopic examination showed multiple confluent cotton-wool spots in both eyes. Swept source-optical coherence tomography presented macular edema in both eyes; optical coherence tomography angiography revealed superficial and deep capillary occlusion in all areas affected by cotton-wool spots; and fluorescein angiography showed vascular walls enhancement, veins dilatation, and capillary leakage. After large doses of intravenously administered glucocorticoid therapy, followed by a cyclophosphamide regimen, best corrected visual acuity returned to 20/20 in both eyes.

Conclusions

This case report presents optical coherence tomography angiography clinical findings in a rare case of dermatomyositis-associated retinopathy, remarking the importance of a multi-imaging approach for a correct diagnosis and treatment of eye injuries, in order to avoid serious complications and permanent sequelae.

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Title: Optical coherence tomography angiography in Purtscher-like retinopathy associated with dermatomyositis: a case report
Authors: D. Vezzola
D. Allegrini
M. R. Romano
L. Pagano
A. Montericcio
P. Fogagnolo
L. M. Rossetti
S. De Cillà
Publication date: 01-12-2019
Publisher: BioMed Central
Keywords: Angiography
Edema
Dermatomyositis
Published in: Journal of Medical Case Reports / Issue 1/2019
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-019-2152-2

At a glance: The STEP trials

Springer Medicine

Optical coherence tomography angiography in Purtscher-like retinopathy associated with dermatomyositis: a case report

Abstract

Purpose

Case presentation

Conclusions

At a glance: The STEP trials

Springer Medicine

Abstract

Purpose

Case presentation

Conclusions

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