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Indian Journal of Pediatrics
Published in: Indian Journal of Pediatrics 6/2020

01-06-2020 | Anemia | Scientific Letter

HbE-Beta Thalassemia with Moyamoya Syndrome: A Rare Association

Authors: Anika Agrawal, Onkar Singh Bhinder, Devendra Mishra, Monica Juneja

Published in: Indian Journal of Pediatrics | Issue 6/2020

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Excerpt

To the Editor: Moyamoya syndrome (MMS), supraclinoid internal carotid artery (ICA) occlusion secondary to hereditary or acquired conditions and resulting in arterial collaterals at the base of the brain, is rarely reported with hematological disorders, except sickle-cell anemia [1]. We report a young girl with thalassemia intermedia and MMS. …
Literature
1.
Oberoi S, Bansal D, Singh P, Marwaha RK. Stroke in a young boy with β-thalassemia intermedia secondary to Moyamoya syndrome. J Pediatr Hematol Oncol. 2010;32:568–70.CrossRef
2.
Tsuda H, Hattori S, Tanabe S, et al. Thrombophilia found in patients with Moyamoya disease. Clin Neurol Neurosurg. 1997;99:S229–33.CrossRef
3.
Borenstain-Ben Yashar V, Barenholz Y, Hy-am E, Rachmilewitz EA, Eldor A. Phosphatidylserine in the outer leaflet of red blood cells from beta- thalassemia patients may explain the chronic hypercoagulable state and thrombotic episodes. Am J Hematol. 1993;44:63–5.CrossRef
4.
Taher A, Isma’eel H, Mehio G, et al. Prevalence of thromboembolic events among 8,860 patients with thalassaemia major and intermedia in the Mediterranean area and Iran. Thromb Haemost. 2006;96:488–91.CrossRef
5.
Doctor PN, Choudhari A, Verma M, Merchant RH. Moyamoya syndrome in hemoglobin E-beta thalassemia: a rare presentation and association. J Postgrad Med. 2018;64:240–2.CrossRef
Metadata
Title
HbE-Beta Thalassemia with Moyamoya Syndrome: A Rare Association
Authors
Anika Agrawal
Onkar Singh Bhinder
Devendra Mishra
Monica Juneja
Publication date
01-06-2020
Publisher
Springer India
Published in
Indian Journal of Pediatrics / Issue 6/2020
Print ISSN: 0019-5456
Electronic ISSN: 0973-7693
DOI
https://doi.org/10.1007/s12098-019-03143-8

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