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01-03-2024 | Abatacept | Letter to Editor

Clinical Characteristics of Pediatric Patients with LRBA Deficiency in Mexico

Authors: Eduardo Liquidano-Perez, Selma Scheffler-Mendoza, Juan Carlos Bustamante-Ogando, Gabriela Lopez-Herrera, Mexican group for Inborn errors of immunity

Published in: Journal of Clinical Immunology | Issue 3/2024

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Tangye SG, Al-Herz W, Bousfiha A, et al. Human inborn errors of immunity: 2022 update on the classification from the international union of immunological societies expert committee. J Clin Immunol. 2022;42(7):1473–507. https://doi.org/10.1007/s10875-022-01289-3.CrossRefPubMedPubMedCentral

Lo B, Zhang K, Lu W, et al. Autoimmune disease. Patients with LRBA deficiency show CTLA4 loss and immune dysregulation responsive to abatacept therapy. Science. 2015;349(6246):436–40. https://doi.org/10.1126/science.aaa1663

Kiykim A, Ogulur I, Dursun E, et al. Abatacept as a long-term targeted therapy for LRBA deficiency. J Allergy Clin Immunol Pract Nov-Dec. 2019;7(8):2790-2800.e15. https://doi.org/10.1016/j.jaip.2019.06.011.CrossRef

Tesch VK, Abolhassani H, Shadur B, et al. Long-term outcome of LRBA deficiency in 76 patients after various treatment modalities as evaluated by the immune deficiency and dysregulation activity (IDDA) score. J Allergy Clin Immunol. 2020;145(5):1452–63. https://doi.org/10.1016/j.jaci.2019.12.896.CrossRefPubMed

Brunner HI, Wong R, Nys M, et al. Paediatric rheumatology international trials organisation (PRINTO) and the pediatric rheumatology collaborative study group (PRCSG). Abatacept: a review of the treatment of polyarticular-course juvenile idiopathic arthritis. Paediatr Drugs. 2020;22(6):653–672. https://doi.org/10.1007/s40272-020-00422-2

Taghizade N, Babayeva R, Kara A, et al. Therapeutic modalities and clinical outcomes in a large cohort with LRBA deficiency and CTLA4 insufficiency. J Allergy Clin Immunol. 2023;S0091–6749(23):01017–25. https://doi.org/10.1016/j.jaci.2023.08.004.CrossRef

Title: Clinical Characteristics of Pediatric Patients with LRBA Deficiency in Mexico
Authors: Eduardo Liquidano-Perez
Selma Scheffler-Mendoza
Juan Carlos Bustamante-Ogando
Gabriela Lopez-Herrera
Mexican group for Inborn errors of immunity
Publication date: 01-03-2024
Publisher: Springer US
Keyword: Abatacept
Published in: Journal of Clinical Immunology / Issue 3/2024
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI: https://doi.org/10.1007/s10875-024-01679-9

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