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01-05-2019 | Brief Report

A case of nasal low-grade non-intestinal-type adenocarcinoma with aberrant CDX2 expression and a novel SYN2-PPARG gene fusion in a 13-year-old girl

Authors: Gwyneth Shook Ting Soon, Kenneth Tou En Chang, Chik Hong Kuick, Fredrik Petersson

Published in: Virchows Archiv | Issue 5/2019

Abstract

We report the first patient (a 13-year-old girl) with a sinonasal low-grade non-intestinal-type adenocarcinoma showing aberrant CDX2 expression both within morular areas and in the tubular component and demonstrate for the first time a SYN2-PPARG gene fusion in this tumor type. The tumor arose from the nasal septum and had not spread beyond the nasal cavity.

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Title: A case of nasal low-grade non-intestinal-type adenocarcinoma with aberrant CDX2 expression and a novel SYN2-PPARG gene fusion in a 13-year-old girl
Authors: Gwyneth Shook Ting Soon
Kenneth Tou En Chang
Chik Hong Kuick
Fredrik Petersson
Publication date: 01-05-2019
Publisher: Springer Berlin Heidelberg
Published in: Virchows Archiv / Issue 5/2019
Print ISSN: 0945-6317
Electronic ISSN: 1432-2307
DOI: https://doi.org/10.1007/s00428-019-02524-w

At a glance: The STEP trials

Springer Medicine

A case of nasal low-grade non-intestinal-type adenocarcinoma with aberrant CDX2 expression and a novel SYN2-PPARG gene fusion in a 13-year-old girl

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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